{"id":19133,"date":"2026-03-18T18:11:33","date_gmt":"2026-03-18T17:11:33","guid":{"rendered":"https:\/\/www.cutislaxa.org\/?p=19133"},"modified":"2026-03-18T18:11:33","modified_gmt":"2026-03-18T17:11:33","slug":"cutis-laxa-acquise","status":"publish","type":"post","link":"https:\/\/www.cutislaxa.org\/fr\/cutis-laxa-acquise\/","title":{"rendered":"Cutis Laxa Acquise"},"content":{"rendered":"<p style=\"text-align: center;\">Pr. Bert CALLEWAERT<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-medium wp-image-18180 aligncenter\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap5-300x186.jpg\" alt=\"\" width=\"300\" height=\"186\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap5-300x186.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap5-768x476.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap5-705x437.jpg 705w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap5.jpg 822w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/p>\n<p class=\"p1\">Ce type de Cutis Laxa reste aujourd\u2019hui encore le plus mal connu. Non inclus dans les formes g\u00e9n\u00e9tiques, il faut n\u00e9anmoins noter une pr\u00e9disposition \u00e0 la d\u00e9velopper ou pas.<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-medium wp-image-18186 aligncenter\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap31-300x184.jpg\" alt=\"\" width=\"300\" height=\"184\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap31-300x184.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap31.jpg 592w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/p>\n<p>Si, depuis longtemps, on parle d\u2019une fa\u00e7on g\u00e9n\u00e9rale de La Cutis Laxa Acquise, on sait aujourd\u2019hui qu\u2019il existe au moins deux formes diff\u00e9rentes selon le contexte dans lequel elle se d\u00e9clare et\u00a0les signes cliniques qu\u2019elle induit.<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-medium wp-image-18174 aligncenter\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap7-300x197.jpg\" alt=\"\" width=\"300\" height=\"197\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap7-300x197.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap7.jpg 613w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/p>\n<p>Contrairement aux formes g\u00e9n\u00e9tiques qui pr\u00e9sentent un d\u00e9faut \u00e0 diverses \u00e9tapes de la \u00ab\u00a0cr\u00e9ation\u00a0\u00bb des fibres \u00e9lastiques, la Cutis Laxa Acquise pr\u00e9sente quant \u00e0 elle une destruction de ces fibres. Il s\u2019agit donc d\u2019un processus diff\u00e9rent issu, soit d\u2019un contexte inflammatoire, soit d\u2019un contexte auto-immunitaire. Il reste beaucoup \u00e0 d\u00e9couvrir sur les m\u00e9canismes de la Cutis Laxa Acquise mais il faut garder en t\u00eate\u00a0:<\/p>\n<ul>\n<li>La morphologie des Fibres Elastiques, la physiopathologie et la pr\u00e9sentation clinique sont li\u00e9es intrins\u00e8quement,<\/li>\n<li>Les r\u00e9ponses inflammatoires \/ l\u2019auto-immunit\u00e9 r\u00e9sultent dans la d\u00e9gradation des fibres \u00e9lastiques<\/li>\n<li>L\u2019infiltration de cellules immunitaires est une signature de la d\u00e9gradation des fibres \u00e9lastiques dans la forme acquise<\/li>\n<li>La prot\u00e9ine Cathepsine V pourrait \u00eatre un nouvel acteur de la d\u00e9gradation des fibres \u00e9lastiques<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Pr. Bert CALLEWAERT Ce type de Cutis Laxa reste aujourd\u2019hui encore le plus mal connu. Non inclus dans les formes g\u00e9n\u00e9tiques, il faut n\u00e9anmoins noter une pr\u00e9disposition \u00e0 la d\u00e9velopper ou pas. Si, depuis longtemps, on parle d\u2019une fa\u00e7on g\u00e9n\u00e9rale de La Cutis Laxa Acquise, on sait aujourd\u2019hui qu\u2019il existe au moins deux formes diff\u00e9rentes [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":6776,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[61,60,66],"tags":[],"class_list":["post-19133","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-quoi-de-neuf","category-recherche","category-recherche-medecine-genetique"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v22.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Cutis Laxa Acquise - CUTIS LAXA INTERNATIONALE<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.cutislaxa.org\/fr\/cutis-laxa-acquise\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Cutis Laxa Acquise - CUTIS LAXA INTERNATIONALE\" \/>\n<meta property=\"og:description\" content=\"Pr. Bert CALLEWAERT Ce type de Cutis Laxa reste aujourd\u2019hui encore le plus mal connu. Non inclus dans les formes g\u00e9n\u00e9tiques, il faut n\u00e9anmoins noter une pr\u00e9disposition \u00e0 la d\u00e9velopper ou pas. 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