{"id":19119,"date":"2026-03-18T17:57:08","date_gmt":"2026-03-18T16:57:08","guid":{"rendered":"https:\/\/www.cutislaxa.org\/?p=19119"},"modified":"2026-03-18T18:00:53","modified_gmt":"2026-03-18T17:00:53","slug":"nouvelle-classification-des-types-de-cutis-laxa","status":"publish","type":"post","link":"https:\/\/www.cutislaxa.org\/fr\/nouvelle-classification-des-types-de-cutis-laxa\/","title":{"rendered":"Nouvelle Classification des Types de Cutis Laxa"},"content":{"rendered":"<p class=\"p1\">Un long travail d\u2019analyse des diff\u00e9rents sympt\u00f4mes de tous les types de Cutis Laxa a \u00e9t\u00e9 men\u00e9 par le Dr A. Beyens. Les dossiers des 192 malades de la cohorte \u00e9tudi\u00e9e par l\u2019\u00e9quipe du Pr Bert Callewaert ainsi que les cas publi\u00e9s dans la litt\u00e9rature ont \u00e9t\u00e9 cribl\u00e9s par l\u2019Intelligence Artificielle (IA) de fa\u00e7on \u00e0 regrouper les sympt\u00f4mes majeurs, tous types confondus.<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone wp-image-18249 aligncenter\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap1-300x185.jpg\" alt=\"\" width=\"347\" height=\"214\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap1-300x185.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap1-768x474.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap1-705x435.jpg 705w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap1.jpg 924w\" sizes=\"auto, (max-width: 347px) 100vw, 347px\" \/><\/p>\n<p class=\"p1\">623 dossiers ont ainsi \u00e9t\u00e9 analys\u00e9s. Les caract\u00e9ristiques cliniques et mol\u00e9culaires, plus de 290 param\u00e8tres ont \u00e9t\u00e9 pris en compte et ont permis de d\u00e9finir 6 groupes partageant des caract\u00e9ristiques cliniques et physiopathologiques\u00a0: la Peau, le syst\u00e8me cardiovasculaire, le syst\u00e8me respiratoire, les os, la glycosylation et les mitochondries. De plus, ces groupes montrent des diff\u00e9rences notables dans la d\u00e9gradation des fibres \u00e9lastiques.<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-medium wp-image-18192 aligncenter\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap3-300x226.jpg\" alt=\"\" width=\"300\" height=\"226\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap3-300x226.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap3-768x579.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap3-705x532.jpg 705w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap3.jpg 899w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/p>\n<p class=\"p1\">Gr\u00e2ce \u00e0 cette \u00e9tude, il est d\u00e9sormais possible de construire un arbre d\u00e9cisionnel qui, en fonction des signes cliniques et pathophysiologiques permet de d\u00e9terminer une suspicion du type de Cutis Laxa dont le malade est atteint.<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-medium wp-image-18222 aligncenter\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap2-300x225.jpg\" alt=\"\" width=\"300\" height=\"225\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap2-300x225.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap2-768x575.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap2-705x528.jpg 705w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap2.jpg 900w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/p>\n<p>Les r\u00e9sultats obtenus ont une fiabilit\u00e9 de pr\u00e8s de 90 %. Cela ne diminue en rien la n\u00e9cessit\u00e9 d\u2019un test g\u00e9n\u00e9tique\/mol\u00e9culaire qui permet de confirmer cette suspicion. Mais, cela permet de mettre en place imm\u00e9diatement la prise en charge et le suivi n\u00e9cessaires selon le type, sans attendre les 6 \u00e0 8 mois n\u00e9cessaires pour obtenir les r\u00e9sultats du test. C\u2019est une avanc\u00e9e significative dans l\u2019am\u00e9lioration du d\u00e9lai de diagnostic et une meilleure prise en charge du malade.<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-medium wp-image-18183 aligncenter\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap4-300x180.jpg\" alt=\"\" width=\"300\" height=\"180\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap4-300x180.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap4-768x460.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap4-705x422.jpg 705w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2026\/03\/CLD-Diap4.jpg 961w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Un long travail d\u2019analyse des diff\u00e9rents sympt\u00f4mes de tous les types de Cutis Laxa a \u00e9t\u00e9 men\u00e9 par le Dr A. Beyens. Les dossiers des 192 malades de la cohorte \u00e9tudi\u00e9e par l\u2019\u00e9quipe du Pr Bert Callewaert ainsi que les cas publi\u00e9s dans la litt\u00e9rature ont \u00e9t\u00e9 cribl\u00e9s par l\u2019Intelligence Artificielle (IA) de fa\u00e7on \u00e0 [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":6776,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[59,61,60,66],"tags":[],"class_list":["post-19119","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-number-mutations-fr","category-quoi-de-neuf","category-recherche","category-recherche-medecine-genetique"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v22.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Nouvelle Classification des Types de Cutis Laxa - CUTIS LAXA INTERNATIONALE<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.cutislaxa.org\/fr\/nouvelle-classification-des-types-de-cutis-laxa\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Nouvelle Classification des Types de Cutis Laxa - CUTIS LAXA INTERNATIONALE\" \/>\n<meta property=\"og:description\" content=\"Un long travail d\u2019analyse des diff\u00e9rents sympt\u00f4mes de tous les types de Cutis Laxa a \u00e9t\u00e9 men\u00e9 par le Dr A. Beyens. Les dossiers des 192 malades de la cohorte \u00e9tudi\u00e9e par l\u2019\u00e9quipe du Pr Bert Callewaert ainsi que les cas publi\u00e9s dans la litt\u00e9rature ont \u00e9t\u00e9 cribl\u00e9s par l\u2019Intelligence Artificielle (IA) de fa\u00e7on \u00e0 [&hellip;]\" \/>\n<meta property=\"og:url\" content=\"https:\/\/www.cutislaxa.org\/fr\/nouvelle-classification-des-types-de-cutis-laxa\/\" \/>\n<meta property=\"og:site_name\" content=\"CUTIS LAXA INTERNATIONALE\" \/>\n<meta property=\"article:publisher\" content=\"https:\/\/www.facebook.com\/CutisLaxaAssociation\/\" \/>\n<meta property=\"article:published_time\" content=\"2026-03-18T16:57:08+00:00\" \/>\n<meta property=\"article:modified_time\" content=\"2026-03-18T17:00:53+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2017\/07\/gene.jpg\" \/>\n\t<meta property=\"og:image:width\" content=\"300\" \/>\n\t<meta property=\"og:image:height\" content=\"300\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/jpeg\" \/>\n<meta name=\"author\" content=\"Marie-Claude\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"\u00c9crit par\" \/>\n\t<meta name=\"twitter:data1\" content=\"Marie-Claude\" \/>\n\t<meta name=\"twitter:label2\" content=\"Dur\u00e9e de lecture estim\u00e9e\" \/>\n\t<meta name=\"twitter:data2\" content=\"3 minutes\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"Article\",\"@id\":\"https:\/\/www.cutislaxa.org\/fr\/nouvelle-classification-des-types-de-cutis-laxa\/#article\",\"isPartOf\":{\"@id\":\"https:\/\/www.cutislaxa.org\/fr\/nouvelle-classification-des-types-de-cutis-laxa\/\"},\"author\":{\"name\":\"Marie-Claude\",\"@id\":\"https:\/\/www.cutislaxa.org\/#\/schema\/person\/2b5e58dca5a6f412607f985f2823d045\"},\"headline\":\"Nouvelle Classification des Types de Cutis Laxa\",\"datePublished\":\"2026-03-18T16:57:08+00:00\",\"dateModified\":\"2026-03-18T17:00:53+00:00\",\"mainEntityOfPage\":{\"@id\":\"https:\/\/www.cutislaxa.org\/fr\/nouvelle-classification-des-types-de-cutis-laxa\/\"},\"wordCount\":276,\"publisher\":{\"@id\":\"https:\/\/www.cutislaxa.org\/#organization\"},\"articleSection\":[\"Mutations\",\"Quoi de neuf\",\"Recherche\",\"Recherche - 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