{"id":13358,"date":"2022-12-27T11:13:05","date_gmt":"2022-12-27T10:13:05","guid":{"rendered":"https:\/\/www.cutislaxa.org\/?p=13358"},"modified":"2023-02-06T09:33:57","modified_gmt":"2023-02-06T08:33:57","slug":"202209-mme-aude-beyens_defauts-structurels-des-proteines-du-tissu","status":"publish","type":"post","link":"https:\/\/www.cutislaxa.org\/fr\/202209-mme-aude-beyens_defauts-structurels-des-proteines-du-tissu\/","title":{"rendered":"Mme Aude Beyens, MD (Ghent, Belgique): D\u00e9fauts structurels des prot\u00e9ines du tissu conjonctif et CL"},"content":{"rendered":"<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-medium wp-image-13339 aligncenter\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115805-2-300x155.jpg\" alt=\"\" width=\"300\" height=\"155\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115805-2-300x155.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115805-2-1030x533.jpg 1030w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115805-2-768x397.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115805-2-1500x775.jpg 1500w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115805-2-705x364.jpg 705w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115805-2.jpg 1530w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/p>\n<p>L\u2019assemblage des fibres \u00e9lastiques, ou \u00e9lastogen\u00e8se, est un processus \u00e0 plusieurs \u00e9tapes compliqu\u00e9es qui est r\u00e9gul\u00e9 de fa\u00e7on tr\u00e8s pr\u00e9cise d\u2019une mani\u00e8re spatiotemporelle et qui d\u00e9pend du signalement et du mecanosensing corrects du facteur de croissance.<\/p>\n<p style=\"text-align: center;\"><img loading=\"lazy\" decoding=\"async\" class=\"alignnone wp-image-13342\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-300x191.jpg\" alt=\"\" width=\"283\" height=\"180\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-300x191.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-1030x655.jpg 1030w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-768x488.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-1536x977.jpg 1536w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-2048x1302.jpg 2048w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-1500x954.jpg 1500w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-705x448.jpg 705w\" sizes=\"auto, (max-width: 283px) 100vw, 283px\" \/> <img loading=\"lazy\" decoding=\"async\" class=\"alignnone wp-image-13345\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-300x189.jpg\" alt=\"\" width=\"286\" height=\"180\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-300x189.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-1030x648.jpg 1030w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-768x483.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-1536x966.jpg 1536w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-2048x1288.jpg 2048w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-1500x943.jpg 1500w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-705x443.jpg 705w\" sizes=\"auto, (max-width: 286px) 100vw, 286px\" \/><\/p>\n<p>&nbsp;<\/p>\n<p>Les d\u00e9fauts mol\u00e9culaires sous-jacents dans les syndromes de la Cutis Laxa affectent la synth\u00e8se et\/ou l\u2019association des fibres \u00e9lastiques associ\u00e9es aux prot\u00e9ines de la matrice extracellulaire.<\/p>\n<p style=\"text-align: center;\"><img loading=\"lazy\" decoding=\"async\" class=\"alignnone wp-image-13348\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-300x213.jpg\" alt=\"\" width=\"253\" height=\"180\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-300x213.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-1030x732.jpg 1030w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-768x546.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-1536x1092.jpg 1536w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-2048x1456.jpg 2048w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-1500x1067.jpg 1500w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-260x185.jpg 260w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-705x501.jpg 705w\" sizes=\"auto, (max-width: 253px) 100vw, 253px\" \/> <img loading=\"lazy\" decoding=\"async\" class=\"alignnone wp-image-13351\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-300x135.jpg\" alt=\"\" width=\"399\" height=\"180\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-300x135.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-1030x464.jpg 1030w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-768x346.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-1536x692.jpg 1536w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-2048x923.jpg 2048w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-1500x676.jpg 1500w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-705x318.jpg 705w\" sizes=\"auto, (max-width: 399px) 100vw, 399px\" \/><\/p>\n","protected":false},"excerpt":{"rendered":"<p>L\u2019assemblage des fibres \u00e9lastiques, ou \u00e9lastogen\u00e8se, est un processus \u00e0 plusieurs \u00e9tapes compliqu\u00e9es qui est r\u00e9gul\u00e9 de fa\u00e7on tr\u00e8s pr\u00e9cise d\u2019une mani\u00e8re spatiotemporelle et qui d\u00e9pend du signalement et du mecanosensing corrects du facteur de croissance. &nbsp; Les d\u00e9fauts mol\u00e9culaires sous-jacents dans les syndromes de la Cutis Laxa affectent la synth\u00e8se et\/ou l\u2019association des fibres [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":13354,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[59,67,61,60,66,64],"tags":[],"class_list":["post-13358","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-number-mutations-fr","category-photos-fr","category-quoi-de-neuf","category-recherche","category-recherche-medecine-genetique","category-rencontres-evenements-et-manifestations"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v22.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Mme Aude Beyens, MD (Ghent, Belgique): D\u00e9fauts structurels des prot\u00e9ines du tissu conjonctif et CL - CUTIS LAXA INTERNATIONALE<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.cutislaxa.org\/202209-mrs-aude-beyens_defects-of-connective-tissue-proteins-and-cl\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Mme Aude Beyens, MD (Ghent, Belgique): D\u00e9fauts structurels des prot\u00e9ines du tissu conjonctif et CL - CUTIS LAXA INTERNATIONALE\" \/>\n<meta property=\"og:description\" content=\"L\u2019assemblage des fibres \u00e9lastiques, ou \u00e9lastogen\u00e8se, est un processus \u00e0 plusieurs \u00e9tapes compliqu\u00e9es qui est r\u00e9gul\u00e9 de fa\u00e7on tr\u00e8s pr\u00e9cise d\u2019une mani\u00e8re spatiotemporelle et qui d\u00e9pend du signalement et du mecanosensing corrects du facteur de croissance. &nbsp; Les d\u00e9fauts mol\u00e9culaires sous-jacents dans les syndromes de la Cutis Laxa affectent la synth\u00e8se et\/ou l\u2019association des fibres [&hellip;]\" \/>\n<meta property=\"og:url\" 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