{"id":16718,"date":"2024-09-18T19:50:26","date_gmt":"2024-09-18T17:50:26","guid":{"rendered":"https:\/\/www.cutislaxa.org\/?p=16718"},"modified":"2024-09-18T19:51:27","modified_gmt":"2024-09-18T17:51:27","slug":"cutis-laxa-que-ocurre","status":"publish","type":"post","link":"https:\/\/www.cutislaxa.org\/es\/cutis-laxa-que-ocurre\/","title":{"rendered":"Cutis Laxa : \u00bfqu\u00e9 ocurre?"},"content":{"rendered":"

Actualizaci\u00f3n de la Cutis Laxa <\/strong><\/p>\n

En el Congreso Mundial de Par\u00eds en junio 2024, se present\u00f3 una actualizaci\u00f3n de los conocimientos de la Cutis Laxa.<\/p>\n

\"\"<\/p>\n

a fisiopatolog\u00eda de la CL est\u00e1 representada por un defecto de las fibras el\u00e1sticas. En el caso de las formas heredadas, se trata de un defecto de s\u00edntesis\/ensamblaje de las fibras el\u00e1sticas cuyo desencadenante es gen\u00e9tico. Cuando se trata de la forma adquirida de Cutis Laxa, el proceso es diferente ya que se trata de una destrucci\u00f3n de fibras el\u00e1sticas que, en principio, son normales.<\/p>\n

Hoy en d\u00eda, se han identificado 18 subtipos en las formas heredadas, contando enfermedades relacionadas como el s\u00edndrome de tortuosidad arterial o el s\u00edndrome de MACS. Estas identificaciones permiten una nueva clasificaci\u00f3n.<\/p>\n

\"\"<\/p>\n

Se encuentran las formas con caracter\u00edsticas esencialmente en el tejido conectivo (Tortuosidad, Piel, Huesos, Enfisema) y aquellas con caracter\u00edsticas esencialmente neurol\u00f3gicas con o sin retraso de crecimiento intrauterino. Esta nueva clasificaci\u00f3n est\u00e1 a\u00fan en fase de validaci\u00f3n. Ser\u00e1 una mejor herramienta de diagn\u00f3stico al integrar los datos cl\u00ednicos, los descubrimientos ultrastructurales y la fisiopatolog\u00eda. Servir\u00e1 de base para nuevas directrices.<\/p>\n

\"\" \"\"<\/p>\n","protected":false},"excerpt":{"rendered":"

Actualizaci\u00f3n de la Cutis Laxa En el Congreso Mundial de Par\u00eds en junio 2024, se present\u00f3 una actualizaci\u00f3n de los conocimientos de la Cutis Laxa. a fisiopatolog\u00eda de la CL est\u00e1 representada por un defecto de las fibras el\u00e1sticas. En el caso de las formas heredadas, se trata de un defecto de s\u00edntesis\/ensamblaje de las […]<\/p>\n","protected":false},"author":2,"featured_media":6594,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[82,74,79,76],"tags":[],"class_list":["post-16718","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-fotos","category-investigacion","category-investigacion-medicina-genetica","category-noticias"],"yoast_head":"\nCutis Laxa : \u00bfqu\u00e9 ocurre? - CUTIS LAXA INTERNATIONALE<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.cutislaxa.org\/es\/cutis-laxa-que-ocurre\/\" \/>\n<meta property=\"og:locale\" content=\"es_ES\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Cutis Laxa : \u00bfqu\u00e9 ocurre? - CUTIS LAXA INTERNATIONALE\" \/>\n<meta property=\"og:description\" content=\"Actualizaci\u00f3n de la Cutis Laxa En el Congreso Mundial de Par\u00eds en junio 2024, se present\u00f3 una actualizaci\u00f3n de los conocimientos de la Cutis Laxa. a fisiopatolog\u00eda de la CL est\u00e1 representada por un defecto de las fibras el\u00e1sticas. 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