{"id":13401,"date":"2022-12-27T11:38:09","date_gmt":"2022-12-27T10:38:09","guid":{"rendered":"https:\/\/www.cutislaxa.org\/?p=13401"},"modified":"2023-02-06T10:53:10","modified_gmt":"2023-02-06T09:53:10","slug":"202209-prof-dr-uwe-kornak_la-via-secretoria-glicosilacion-y-cl","status":"publish","type":"post","link":"https:\/\/www.cutislaxa.org\/es\/202209-prof-dr-uwe-kornak_la-via-secretoria-glicosilacion-y-cl\/","title":{"rendered":"Prof. Dr. Uwe Kornak, MD (G\u00f6ttingen, Alemania): La V\u00eda Secretoria, Glicosilaci\u00f3n y CL"},"content":{"rendered":"<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-medium wp-image-13378 aligncenter\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_122526-300x206.jpg\" alt=\"\" width=\"300\" height=\"206\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_122526-300x206.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_122526-1030x706.jpg 1030w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_122526-768x526.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_122526-1536x1052.jpg 1536w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_122526-1500x1028.jpg 1500w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_122526-705x483.jpg 705w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_122526.jpg 2004w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/p>\n<p>Las prote\u00ednas secretadas y las prote\u00ednas de membrana deben pasar por la v\u00eda secretora, que no solo es responsable del transporte al compartimento celular correcto, sino tambi\u00e9n de la maduraci\u00f3n y modificaci\u00f3n de estas prote\u00ednas. La parte central de esta v\u00eda secretora es el compartimiento Golgi que consiste en varias bolsas de membrana que se asemejan a panqueques (cisternae).<\/p>\n<p style=\"text-align: center;\"><img loading=\"lazy\" decoding=\"async\" class=\"alignnone wp-image-13381\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_123245-300x193.jpg\" alt=\"\" width=\"280\" height=\"180\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_123245-300x193.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_123245-1030x662.jpg 1030w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_123245-768x493.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_123245-1536x987.jpg 1536w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_123245-2048x1316.jpg 2048w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_123245-1500x964.jpg 1500w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_123245-705x453.jpg 705w\" sizes=\"auto, (max-width: 280px) 100vw, 280px\" \/> <img loading=\"lazy\" decoding=\"async\" class=\"alignnone wp-image-13384\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_124515-2-300x204.jpg\" alt=\"\" width=\"265\" height=\"180\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_124515-2-300x204.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_124515-2-1030x701.jpg 1030w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_124515-2-768x522.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_124515-2-1500x1020.jpg 1500w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_124515-2-705x480.jpg 705w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_124515-2.jpg 1507w\" sizes=\"auto, (max-width: 265px) 100vw, 265px\" \/><\/p>\n<p>Una modificaci\u00f3n importante es la glicosilaci\u00f3n, que se ha encontrado modificada en todo un grupo de enfermedades Cutis Laxa, tambi\u00e9n llamadas enfermedades cong\u00e9nitas de la glicosilaci\u00f3n (CDG).<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-medium wp-image-13387 aligncenter\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_125310-300x190.jpg\" alt=\"\" width=\"300\" height=\"190\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_125310-300x190.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_125310-1030x653.jpg 1030w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_125310-768x487.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_125310-705x447.jpg 705w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_125310.jpg 1397w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Las prote\u00ednas secretadas y las prote\u00ednas de membrana deben pasar por la v\u00eda secretora, que no solo es responsable del transporte al compartimento celular correcto, sino tambi\u00e9n de la maduraci\u00f3n y modificaci\u00f3n de estas prote\u00ednas. La parte central de esta v\u00eda secretora es el compartimiento Golgi que consiste en varias bolsas de membrana que se [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":13375,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[77,82,74,79,73,76],"tags":[],"class_list":["post-13401","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-encuentros-acontecimientos-y-manifestaciones","category-fotos","category-investigacion","category-investigacion-medicina-genetica","category-number-mutations-es","category-noticias"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v22.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Prof. Dr. Uwe Kornak, MD (G\u00f6ttingen, Alemania): La V\u00eda Secretoria, Glicosilaci\u00f3n y CL - CUTIS LAXA INTERNATIONALE<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.cutislaxa.org\/202209-prof-dr-uwe-kornak_the-secretory-pathway-glycosylation-and-cutis-laxa\/\" \/>\n<meta property=\"og:locale\" content=\"es_ES\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Prof. Dr. Uwe Kornak, MD (G\u00f6ttingen, Alemania): La V\u00eda Secretoria, Glicosilaci\u00f3n y CL - CUTIS LAXA INTERNATIONALE\" \/>\n<meta property=\"og:description\" content=\"Las prote\u00ednas secretadas y las prote\u00ednas de membrana deben pasar por la v\u00eda secretora, que no solo es responsable del transporte al compartimento celular correcto, sino tambi\u00e9n de la maduraci\u00f3n y modificaci\u00f3n de estas prote\u00ednas. La parte central de esta v\u00eda secretora es el compartimiento Golgi que consiste en varias bolsas de membrana que se [&hellip;]\" \/>\n<meta property=\"og:url\" content=\"https:\/\/www.cutislaxa.org\/202209-prof-dr-uwe-kornak_the-secretory-pathway-glycosylation-and-cutis-laxa\/\" \/>\n<meta property=\"og:site_name\" content=\"CUTIS LAXA INTERNATIONALE\" \/>\n<meta property=\"article:publisher\" content=\"https:\/\/www.facebook.com\/CutisLaxaAssociation\/\" \/>\n<meta property=\"article:published_time\" content=\"2022-12-27T10:38:09+00:00\" \/>\n<meta property=\"article:modified_time\" content=\"2023-02-06T09:53:10+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/UWE.jpg\" \/>\n\t<meta property=\"og:image:width\" content=\"156\" \/>\n\t<meta property=\"og:image:height\" content=\"174\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/jpeg\" \/>\n<meta name=\"author\" content=\"Marie-Claude\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Escrito por\" \/>\n\t<meta name=\"twitter:data1\" content=\"Marie-Claude\" \/>\n\t<meta name=\"twitter:label2\" content=\"Tiempo de lectura\" \/>\n\t<meta name=\"twitter:data2\" content=\"2 minutos\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"Article\",\"@id\":\"https:\/\/www.cutislaxa.org\/202209-prof-dr-uwe-kornak_the-secretory-pathway-glycosylation-and-cutis-laxa\/#article\",\"isPartOf\":{\"@id\":\"https:\/\/www.cutislaxa.org\/202209-prof-dr-uwe-kornak_the-secretory-pathway-glycosylation-and-cutis-laxa\/\"},\"author\":{\"name\":\"Marie-Claude\",\"@id\":\"https:\/\/www.cutislaxa.org\/#\/schema\/person\/2b5e58dca5a6f412607f985f2823d045\"},\"headline\":\"Prof. Dr. Uwe Kornak, MD (G\u00f6ttingen, Alemania): La V\u00eda Secretoria, Glicosilaci\u00f3n y CL\",\"datePublished\":\"2022-12-27T10:38:09+00:00\",\"dateModified\":\"2023-02-06T09:53:10+00:00\",\"mainEntityOfPage\":{\"@id\":\"https:\/\/www.cutislaxa.org\/202209-prof-dr-uwe-kornak_the-secretory-pathway-glycosylation-and-cutis-laxa\/\"},\"wordCount\":115,\"publisher\":{\"@id\":\"https:\/\/www.cutislaxa.org\/#organization\"},\"articleSection\":[\"Encuentros, Acontecimientos y Manifestaciones\",\"fotos\",\"Investigaci\u00f3n\",\"Investigaci\u00f3n- Medicina - 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