{"id":13365,"date":"2022-12-27T11:17:45","date_gmt":"2022-12-27T10:17:45","guid":{"rendered":"https:\/\/www.cutislaxa.org\/?p=13365"},"modified":"2023-02-06T10:53:53","modified_gmt":"2023-02-06T09:53:53","slug":"202209-sra-aude-beyens_defectos-estructurales-de-las-proteinas-del-tejido","status":"publish","type":"post","link":"https:\/\/www.cutislaxa.org\/es\/202209-sra-aude-beyens_defectos-estructurales-de-las-proteinas-del-tejido\/","title":{"rendered":"Sra Aude Beyens, MD (Ghent, B\u00e9lgica): Defectos estructurales de las prote\u00ednas del tejido conjuntivo y CL"},"content":{"rendered":"<p>El ensamblaje de las fibras el\u00e1sticas, o elastog\u00e9nesis, es un proceso de varias etapas complicadas que se regula de manera muy precisa de una manera espacio-temporal y que depende de la descripci\u00f3n y mecanosensing correctas del factor de crecimiento.<\/p>\n<p style=\"text-align: center;\"><img loading=\"lazy\" decoding=\"async\" class=\"alignnone wp-image-13343\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-300x191.jpg\" alt=\"\" width=\"283\" height=\"180\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-300x191.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-1030x655.jpg 1030w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-768x488.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-1536x977.jpg 1536w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-2048x1302.jpg 2048w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-1500x954.jpg 1500w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_115846-705x448.jpg 705w\" sizes=\"auto, (max-width: 283px) 100vw, 283px\" \/> <img loading=\"lazy\" decoding=\"async\" class=\"alignnone wp-image-13346\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-300x189.jpg\" alt=\"\" width=\"286\" height=\"180\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-300x189.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-1030x648.jpg 1030w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-768x483.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-1536x966.jpg 1536w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-2048x1288.jpg 2048w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-1500x943.jpg 1500w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_120616-705x443.jpg 705w\" sizes=\"auto, (max-width: 286px) 100vw, 286px\" \/><\/p>\n<p>Los defectos moleculares subyacentes en los s\u00edndromes de la Cutis Laxa afectan la s\u00edntesis y\/o asociaci\u00f3n de las fibras el\u00e1sticas asociadas a las prote\u00ednas de la matriz extracelular.<\/p>\n<p style=\"text-align: center;\"><img loading=\"lazy\" decoding=\"async\" class=\"alignnone wp-image-13349\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-300x213.jpg\" alt=\"\" width=\"253\" height=\"180\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-300x213.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-1030x732.jpg 1030w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-768x546.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-1536x1092.jpg 1536w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-2048x1456.jpg 2048w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-1500x1067.jpg 1500w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-260x185.jpg 260w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121614-705x501.jpg 705w\" sizes=\"auto, (max-width: 253px) 100vw, 253px\" \/> <img loading=\"lazy\" decoding=\"async\" class=\"alignnone wp-image-13352\" src=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-300x135.jpg\" alt=\"\" width=\"399\" height=\"180\" srcset=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-300x135.jpg 300w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-1030x464.jpg 1030w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-768x346.jpg 768w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-1536x692.jpg 1536w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-2048x923.jpg 2048w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-1500x676.jpg 1500w, https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/IMG_20220915_121718-705x318.jpg 705w\" sizes=\"auto, (max-width: 399px) 100vw, 399px\" \/><\/p>\n","protected":false},"excerpt":{"rendered":"<p>El ensamblaje de las fibras el\u00e1sticas, o elastog\u00e9nesis, es un proceso de varias etapas complicadas que se regula de manera muy precisa de una manera espacio-temporal y que depende de la descripci\u00f3n y mecanosensing correctas del factor de crecimiento. Los defectos moleculares subyacentes en los s\u00edndromes de la Cutis Laxa afectan la s\u00edntesis y\/o asociaci\u00f3n [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":13355,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[77,82,74,79,73,76],"tags":[],"class_list":["post-13365","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-encuentros-acontecimientos-y-manifestaciones","category-fotos","category-investigacion","category-investigacion-medicina-genetica","category-number-mutations-es","category-noticias"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v22.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Sra Aude Beyens, MD (Ghent, B\u00e9lgica): Defectos estructurales de las prote\u00ednas del tejido conjuntivo y CL - CUTIS LAXA INTERNATIONALE<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.cutislaxa.org\/202209-mrs-aude-beyens_defects-of-connective-tissue-proteins-and-cl\/\" \/>\n<meta property=\"og:locale\" content=\"es_ES\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Sra Aude Beyens, MD (Ghent, B\u00e9lgica): Defectos estructurales de las prote\u00ednas del tejido conjuntivo y CL - CUTIS LAXA INTERNATIONALE\" \/>\n<meta property=\"og:description\" content=\"El ensamblaje de las fibras el\u00e1sticas, o elastog\u00e9nesis, es un proceso de varias etapas complicadas que se regula de manera muy precisa de una manera espacio-temporal y que depende de la descripci\u00f3n y mecanosensing correctas del factor de crecimiento. Los defectos moleculares subyacentes en los s\u00edndromes de la Cutis Laxa afectan la s\u00edntesis y\/o asociaci\u00f3n [&hellip;]\" \/>\n<meta property=\"og:url\" content=\"https:\/\/www.cutislaxa.org\/202209-mrs-aude-beyens_defects-of-connective-tissue-proteins-and-cl\/\" \/>\n<meta property=\"og:site_name\" content=\"CUTIS LAXA INTERNATIONALE\" \/>\n<meta property=\"article:publisher\" content=\"https:\/\/www.facebook.com\/CutisLaxaAssociation\/\" \/>\n<meta property=\"article:published_time\" content=\"2022-12-27T10:17:45+00:00\" \/>\n<meta property=\"article:modified_time\" content=\"2023-02-06T09:53:53+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/www.cutislaxa.org\/wp-content\/uploads\/2023\/01\/AUDE.jpg\" \/>\n\t<meta property=\"og:image:width\" content=\"224\" \/>\n\t<meta property=\"og:image:height\" content=\"209\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/jpeg\" \/>\n<meta name=\"author\" content=\"Marie-Claude\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Escrito por\" \/>\n\t<meta name=\"twitter:data1\" content=\"Marie-Claude\" \/>\n\t<meta name=\"twitter:label2\" content=\"Tiempo de lectura\" \/>\n\t<meta name=\"twitter:data2\" content=\"2 minutos\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"Article\",\"@id\":\"https:\/\/www.cutislaxa.org\/202209-mrs-aude-beyens_defects-of-connective-tissue-proteins-and-cl\/#article\",\"isPartOf\":{\"@id\":\"https:\/\/www.cutislaxa.org\/202209-mrs-aude-beyens_defects-of-connective-tissue-proteins-and-cl\/\"},\"author\":{\"name\":\"Marie-Claude\",\"@id\":\"https:\/\/www.cutislaxa.org\/#\/schema\/person\/2b5e58dca5a6f412607f985f2823d045\"},\"headline\":\"Sra Aude Beyens, MD (Ghent, B\u00e9lgica): Defectos estructurales de las prote\u00ednas del tejido conjuntivo y CL\",\"datePublished\":\"2022-12-27T10:17:45+00:00\",\"dateModified\":\"2023-02-06T09:53:53+00:00\",\"mainEntityOfPage\":{\"@id\":\"https:\/\/www.cutislaxa.org\/202209-mrs-aude-beyens_defects-of-connective-tissue-proteins-and-cl\/\"},\"wordCount\":94,\"publisher\":{\"@id\":\"https:\/\/www.cutislaxa.org\/#organization\"},\"articleSection\":[\"Encuentros, Acontecimientos y Manifestaciones\",\"fotos\",\"Investigaci\u00f3n\",\"Investigaci\u00f3n- Medicina - 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